Table 1: Demographic data is presented for the study participants, along with frequency of immunodeficiency comorbidities, average immunoglobulin D (IgD) and frequency of elevated IgD.
Characteristics | Result N = 87 |
Age onset of symptoms, years (range) | 2.2 ± 1.7 (0.2-8) |
Age at diagnosis, years (range) | 3.9 ± 2.5 (1-9) |
Female, n, % | 43, 49% |
Race, n, % | |
White | 79, 90.8% |
Black | 6, 6.9% |
Hispanic | 1, 1.1% |
Asian | 1, 1.1% |
Associated conditions, n, % | |
THI | 4, 4.6% |
SAD | 4, 4.6% |
MBL deficiency | 1, 1.1% |
MEFV heterozygous mutation | 3, 3.4% |
IgD, mg/dl, (range) | 6.8 ± 9.7, (0.69 to 44.43) |
Elevated IgD, % | 10.80% |
S. pneumoniae antibody, % protective | |
Pre | 45.7% ± 17.0% |
Post Prevnar® immunization | 69.3% ± 26.1% |
Post Pneumovax® immunization | 80.0% ± 18.5% |