Table 3: Multi-tumour and carotid paragangliomas (CPG) related tosyndromes and diseases. Literature review.
N patients |
CPG & Syndromes - Genetic + / - / NR |
CPG & Diseases - Genetic + / - / NR |
Total |
With multi-tumours Without multi-tumours Not reported |
4 (23.5%)*1/0/3 6 (35.3%). 2/0/4 7 (41.2%) 0/0/7 |
15 (75%)**9/0/6 5 (25%) 1/2/2 0 |
19 (51.4%) 10/0/9 11 (29.7%) 3/2/6 7 (18.9%) 0/0/7 |
Total cases |
17 |
20 |
37 |
*Included bilateral CPG, other PGs and other tumour unrelated to these syndromes.
**Included bilateral CPG, other PGs/PHEOs and other tumour unrelated to these diseases (e.g., adenomas).
NR: Not reported.
CPG & Syndromes vs. CPG & Diseases: p < 0.001 (chi-squared test).