Table 2: Outcomes of non-cardiac thoracic malformations with associated anomalies and co-morbidities.
|
Non-cardiac thoracic malformations (n = 25) |
Type of cases |
Number of cases |
Outcomes |
Associated anomalies and co-morbidities |
|
Congenital pulmonary airway malformation (n = 8) |
Type 1 (n = 2) |
1 |
Termination at the 20th gestational week |
Hydrops, anhydramnios |
|
|
|
1 |
Unremarkable in neonatal period/Asymptomatic |
Hydrops, anhydramnios |
|
|
|
|
|
|
|
|
Type 2 (n = 2) |
2 |
Successful neonatal surgery at the 6th months of life, followed until 2 years of age |
|
|
|
Type 3 (n=4) |
4 |
In utero regression at the third trimester/Asymptomatic |
|
|
Pleural effusion (n = 4) |
|
2 |
Intrauterine exitus |
Hydrops |
|
|
|
1 |
Survived (3 months follow-up) |
Parvovirus |
|
|
|
1 |
Survived (6 months follow-up) |
Trisomy 21 |
|
Pulmonary hypoplasia (n = 4) |
|
1 |
Exitus soon after birth |
Achondrogenesis |
|
|
|
1 |
Exitus soon after birth |
Thanatophoric dysplasia |
|
|
|
1 |
Intrauterine exitus |
Anhydramnios |
|
|
|
1 |
Postnatal exitus at the 3rd day of life |
Bilateral multicystic dysplastic kidney |
|
Congenital diaphragmatic hernia (n = 4) |
|
1 |
Postnatal exitus at the first week of life |
Ventricular septal defect |
|
|
|
1 |
Surgery within 24 hours of life, followed until 2 years of age |
|
|
|
|
1 |
Exitus after surgery at the second day of life |
|
|
|
|
1 |
Termination of pregnancy at the 16th gestational week |
|
|
Bronchopulmonary sequestration (n = 3) |
|
3 |
Regression (at the 30th, 33rd, 36th gestational weeks ) |
|
|
Congenital lymphangioma (n = 1) |
|
1 |
Cured with Bleomycin therapy at the 6th month of life |
|
|
Pectus excavatum (n = 1) |
|
1 |
No cardiopulmonary complication |
Mild ventriculomegaly Perimembranous ventricular septal defect Hypospadias |