Table 1: Clinical course of patient with DIPNECH before and after treatment with SSA.
FVC [%] | FEV1 [%] | DLco [%] | Symptoms | Lung CT | Management | |
2011 | 85 | 88 | 57 | Present | Numerous small nodules | Surgical procedure |
2014 | 75 | 80 | 46 | Present | GC | |
2015 | 81 | 85 | n.d. | Present + GC side effects | ||
2016 | 82 | 83 | 54 | Present | Progression | Surgical procedure |
79 | 60 | 48 | Absent | SSA | ||
2017 | 61 | 68 | n.d. | Absent | Stagnation |
GC: Glucocorticoids; SSA: Somatostatin Analogues; n.d.: no data.