Table 1: Clinical course of patient with DIPNECH before and after treatment with SSA.

FVC [%] FEV1 [%] DLco [%] Symptoms Lung CT Management
2011 85 88 57 Present Numerous small nodules Surgical procedure
2014 75 80 46 Present GC
2015 81 85 n.d. Present + GC side effects
2016 82 83 54 Present Progression Surgical procedure
79 60 48 Absent SSA
2017 61 68 n.d. Absent Stagnation

GC: Glucocorticoids; SSA: Somatostatin Analogues; n.d.: no data.