Table 1: Comparison of clinical presentation according to different studies.

Authors

 « café au lait » skin pigmentation 

Endocrinopathy

Fibrous dysplasia  

Jung, et al. [6] Strasbourg, France

Yes

No

No

Ezzine, et al. [4] Sousse, Tunisie

Yes

Yes

Yes

Boudriga, et al. [5] Sousse, Tunisia

Yes

Yes

Yes

Our study, Fez Morocco

No

Yes

Yes