Table 1: Classification system for RSVA.

Type

Sakakibara classification

Modified Sakakibara classification

I

 

Originating from left part of right coronary sinus; protruding into conus of right ventricle, just beneath commissure of right and left pulmonary valves.

Protrusion and rupture into right ventricle just beneath pulmonary valve.

II

 

Originating from central part of right coronary sinus; protruding into right ventricle; penetrating crista supraventricularis.

Penetration and rupture into or just beneath crista supraventricularis of right ventricle.

IIIv

 

Originating from posterior part of right coronary sinus; protruding into right ventricle, just beneath septal leaflet of tricuspid valve; penetrating membranous septum.

Penetration and rupture into right ventricle adjacent to or at tricuspid annulus.

 

IIIa

Originating from posterior part of right coronary sinus; protruding into right atrium, near commissure of septal and anterior leaflets of tricuspid valve.

Penetration and rupture into right atrium adjacent to or at tricuspid annulus.

IV

             

Originating from right part of noncoronary sinus; protruding into right atrium, near septal leaflets of tricuspid valve.

Protrusion and rupture into right atrium.

 

V

 

Other rare conditions (eg, rupture into left atrium, pulmonary artery, left ventricle, or other structures).