Table 2: Summary
of clinical characteristics.
|
Characteristic |
FMF (n = 10) |
|
|
Median
age at onset symptoms in years (range) |
29.5
(17-68) |
|
|
Median
age at diagnosis in years (range) |
45
(18-71) |
|
|
Sex |
Male |
8 |
|
|
Female |
2 |
|
Median
duration of skin lesions before diagnosis in years (range) |
11
(1-19) |
|
|
Type
of skin lesions at diagnosis |
Patches |
7 |
|
|
Infiltrated
plaques |
9 |
|
|
Follicular
prominence |
5 |
|
|
Follicular
papules |
3 |
|
|
Follicular
pustules |
1 |
|
|
Alopecia |
8 |
|
|
Nodules |
5 |
|
|
Tumors |
1 |
|
|
Erythroderma |
0 |
|
|
Cysts/comedones |
4 |
|
|
Pruritis |
5 |
|
Location
of skin lesions |
Head
and face |
8 |
|
|
Upper
extremities |
9 |
|
|
Lower
extremities |
8 |
|
|
Trunk |
8 |
|
|
Genital |
3 |
|
|
Buttocks |
4 |
|
Clinical
stage at diagnosis |
Patch-plaque
(T1-2) |
9 |
|
|
Tumor
(T3) |
1 |
|
|
Nodal
involvement |
1 |
|
|
Visceral
involvement |
0 |
|
Progression |
5 |
|