Case

Case 2

Case 3

Case 4

Case 5

Case 6

WBC (/μl)

6300

4700

5700

4200

6700

7200

Hb (g/dl)

10.7

8.4

7.5

7.7

12.9

11

Ht (%)

32.5

24.5

22.2

22.9

37.8

34.5

Ret. (%)

28

63

24

68

33

12

Plt (×104/μl)

17.7

22.9

26.5

21.2

9.6

16.6

NCC (×104/μl)

1.85

11.5

17

16

Dry tap

3.76

Mgk (/μl)

18.75

56.25

81.25

12.5

Dry tap

0

M/E

3

1.3

2.8

4

Dry tap

1.8

Chromosome

46,XX,del(9)(q?)

45,X-Y

46,XX

46,XX

Not done

46,XX

H in stool

( - )

( - )

( - )

( - )

Not done

Ferritin (ng/ml)

266

629

2185

451

79

81

Albumin (g/dl)

3.7

3.4

4.2

3.7

4.5

4.1

Cholesterol (mg/dl)

239

137

137

166

214

226

LDH (U/L)

1792

272

469

1100

237

250

Haptoglobin

<10

<10

73

<10

48

Not done

ParvovirusB19IgM antibody

( - )

( - )

( - )

( - )

( - )

( - )

ParvovirusB19IgG antibody

3.46

5.97

1.63

7.36

6.09

7.24

Anti-nuclear antibody(ANA)

( + )

( - )

( - )

( - )

( + )

( + )

Immunological abnormality

IndCoombs(+)ANA(+)

S-IL2R(684)

DCoombs(±)S-IL2R(546)

S-IL2R(423)

S-IL2R(1330)ANA(+)

S-IL2R(734)ANA(+)

Abnormal immunoglobulin

IgG(625)

IgG(850)IgA(20)

IgM(30)

IgG(652)

Not done

IgG(591)IgA(99)

Others before hospitalization

FT3(0.97)FT4(0.66)

Pollenosis

Skin rash with eosinophilia

β2MG(6.4)

Skin rash by antibiotics

Asthma

S- IL2R: Soluble IL-2 Receptor, WBC: White Blood Cell, Hb: Hemoglobin, Ht: Hematocrit, Ret: Reticulocyte, Plt: Platelet, NCC: Nuclear Cell Count, Mgk: Megakaryocyte, M/E: Myelocyte-Erythrocyte Ratio

FT3, free T3; FT4, free T4; β2MG, β2microglobulin)

 

 

 

 

 

 

(Within normal limit: IgG, 870mg/dl; IgA, 110mg/dl; IgM, 35mg/dl; albumin, 3.9g/dl; cholesterol, 150mg/dl; LDH, 229U/L; ferritin, 200ng/ml; S-IL2R, 519U/ml; FT3, 2.30pg/ml;

FT4, ; 0.80ng/ml; β2MG, 2.0mg/L)

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

   Table 1: Picture of the cases