Table 2: Dedifferentiated leiomyosarcoma of the uterus.

Publication
Clinical information
Histological characteristis
Immunohistchemistry
Year Author Age Size Therapy Metastasis Status (*) SMA Des Calp h-Cal CD10 CK ER PgR
1991 Fukuda [4] 48 8 cm SH+USO lung, liver Dead (11 m) epithlioid cells, OLGC NA - NA NA NA + NA NA
2007 Iihara [8] 48 14 cm UAE+SH lung, brain Dead (20 m) bizzare cells + - NA + NA NA - -
2011 Chen [5] 59 6.8 cm TBH+BSO none Alive (28 m) NA + NA NA NA NA - NA NA
2012 Chen [5] 80 18 cm excision NA Dead (12 m) NA + NA NA NA NA - NA NA
2012 Rawish [7] 48 18 cm SH+BSO+CT serosa, RP Alive (8 m) osteoids - - NA - NA NA focal focal
2016 Nosaka 63 12.4 cm SH+CT lung Alive (9 m) bizzare cells + - focal - + - - -

SH: Simple Hysterectomy, USO: Unilateral Salpingo-Oophorectomy, UAE: Uterine Arterial Embolization, TBH: Total abdominal Hysterectomy, BSO: Bilateral Salpingo-Ooophorectomy, CT: Chemotherapy, NA: Not Available, RP: Retroperitoneum, OLGC: Osteoclast-like Giant Cells, SMA: α-SMA, Des: Desmin, Calp: Calponin, h-Cal: h-Caldesmon, CK: Cytokeratin, ER: Estrogen Receptor, PgR: Progesteron Receptor.

*Survival after presentation or first surgery.