Table 2: Dedifferentiated leiomyosarcoma of the uterus.
Publication | Histological characteristis | ||||||||||||||
Year | Author | Age | Size | Therapy | Metastasis | Status (*) | SMA | Des | Calp | h-Cal | CD10 | CK | ER | PgR | |
1991 | Fukuda [4] | 48 | 8 cm | SH+USO | lung, liver | Dead (11 m) | epithlioid cells, OLGC | NA | - | NA | NA | NA | + | NA | NA |
2007 | Iihara [8] | 48 | 14 cm | UAE+SH | lung, brain | Dead (20 m) | bizzare cells | + | - | NA | + | NA | NA | - | - |
2011 | Chen [5] | 59 | 6.8 cm | TBH+BSO | none | Alive (28 m) | NA | + | NA | NA | NA | NA | - | NA | NA |
2012 | Chen [5] | 80 | 18 cm | excision | NA | Dead (12 m) | NA | + | NA | NA | NA | NA | - | NA | NA |
2012 | Rawish [7] | 48 | 18 cm | SH+BSO+CT | serosa, RP | Alive (8 m) | osteoids | - | - | NA | - | NA | NA | focal | focal |
2016 | Nosaka | 63 | 12.4 cm | SH+CT | lung | Alive (9 m) | bizzare cells | + | - | focal | - | + | - | - | - |
SH: Simple Hysterectomy, USO: Unilateral Salpingo-Oophorectomy, UAE: Uterine Arterial Embolization, TBH: Total abdominal Hysterectomy, BSO: Bilateral Salpingo-Ooophorectomy, CT: Chemotherapy, NA: Not Available, RP: Retroperitoneum, OLGC: Osteoclast-like Giant Cells, SMA: α-SMA, Des: Desmin, Calp: Calponin, h-Cal: h-Caldesmon, CK: Cytokeratin, ER: Estrogen Receptor, PgR: Progesteron Receptor.
*Survival after presentation or first surgery.