Carotid paragangliomas (CPG) related tosyndromes and diseases. Literature review.

Table 2: Carotid paragangliomas (CPG) related tosyndromes and diseases. Literature review.

CPG & Syndromes

CPG & Diseases

Total

Cases, n

Gender, male/female

Age, mean^*

Age, mean (male/female)

CPG bilateral, n (%)

CPG malignant, n (%)

CPG functional, n (%)

Other PGs/PHEO, n (%)

Other tumours, n (%)^**

Genetic studies (positive)

CPG surgery, n/total

Mortality reported

3/3 (11 NR)

29.5 + 5.0 (11 NR)

28.3/30.7

2 (11.8%)

1 (5.9%)

6 (35.3%)

3/3 (14 NR)

6/7 (10 NR)

6/12 (2 NR)

46.1 + 3.6 (2 NR)

45.8/46.1

8 (40.0%)

5 (25.0%)

8 (40.0%)

7/9 (11 NR)

13/15 (5 NR)

2 cases

9/15 (13 NR)

41.9 + 3.9 (13 NR)

40.0/43.1

10 (27.0%)

1 (2.7%)

11 (29.7%)

8 (21.6%)

10/12 (25 NR)

19/22 (15 NR)

2 cases

CPG: Carotid Paraganglioma; PHEO: Pheochromocytoma; NR: Not reported.
*Age in CPG & Syndromes vs. CPG & Diseases: p = 0.012 (Student's t-test).
**Unrelated to these syndromes or diseases.