Table 3: Multi-tumour and carotid paragangliomas (CPG) related tosyndromes and diseases. Literature review.

N patients

CPG & Syndromes - Genetic + / - / NR

CPG & Diseases - Genetic + / - / NR

Total

With multi-tumours

Without multi-tumours

Not reported

4 (23.5%)*1/0/3

6 (35.3%). 2/0/4

7 (41.2%) 0/0/7

15 (75%)**9/0/6

5 (25%) 1/2/2

0

19 (51.4%) 10/0/9

11 (29.7%) 3/2/6

7 (18.9%) 0/0/7

Total cases

17

20

37

*Included bilateral CPG, other PGs and other tumour unrelated to these syndromes.
**Included bilateral CPG, other PGs/PHEOs and other tumour unrelated to these diseases (e.g., adenomas).
NR: Not reported.
CPG & Syndromes vs. CPG & Diseases: p < 0.001 (chi-squared test).