Table 2: Presenting symptoms.

 

n (%)

Skin tightness

 

49 (89.1%)

Dyspnea

47 (85.4%)

Raynaud’s phenomena

46 (83.6%)

Dysphagia

23 (41.8%)

Cough

16 (29.1%)

Dyspnea grade

1

7 (12.7%)

2

32 (58.2%)

3

7 (12.7%)

4

1 (1.8%)