Citation

Park J, Sehgal V (2019) Clinical Conundrums in Diagnosis and Management of Multisystem Langerhans Cell Histiocytosis. Int Arch Intern Med 3:020. doi.org/10.23937/2643-4466/1710020

Copyright

© 2019 Park J, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

CASE REPORT | OPEN ACCESS DOI: 10.23937/2643-4466/1710020

Clinical Conundrums in Diagnosis and Management of Multisystem Langerhans Cell Histiocytosis

Jun Park, MD* and Vishal Sehgal, MD

St. Vincent Hospital Indianapolis, Indiana, USA

Abstract

Background/Aims

Langerhans Cell Histiocytosis (LCH) is a rare disorder with an incident of 1.8 cases per 1,000,000. It involves granulomatous deposits in multiple organs, leading to a wide variety of manifestations such as bone lesions, pulmonary nodules, pituitary lesions, and skin lesions. With mucocutaneous manifestation, it is often diagnosed in childhood, typically making LCH a childhood disease. However, due to the involvement of multiple organ systems and variable clinical courses, if not diagnosed during childhood, the patients with LCH often suffer from delayed diagnosis and treatments as adults.