Free Floating Ball Thrombus in the Left Atrium in a Child with Restrictive Cardiomyopathy
Department of Pediatrics, The University of Jordan, Jordan
*Corresponding author: Iyad AL-Ammouri, MD, Associate professor of pediatric cardiology, Department of Pediatrics, School of Medicine, The University of Jordan, Queen Rania street, Amman 11942, Jordan, Tel: 0096-2653-536-66 ext. 2767, Mobile: 0096-79906-0180, Fax: +96265-300-820, E-mail: Iyad72@hotmail.com
Clin Med Img Lib, CMIL-2-055, (Volume 2, Issue 8); ISSN: 2474-3682
Published: November 15, 2016
Citation: Al-Ammouri I (2016) Free Floating Ball Thrombus in the Left Atrium in a Child with Restrictive Cardiomyopathy. Clin Med Img Lib 2:055.
Copyright: © 2016 Al-Ammouri I. This is an open-access content distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
A large free floating ball thrombus was diagnosed in an 8-year-old girl with severe restrictive cardiomyopathy following transient loss of vision. The thrombus developed despite therapeutic anticoagulation. The child died two days later with a massive embolic stroke.
Idiopathic restrictive cardiomyopathy is a rare disease in children and generally has poor prognosis. The severely dilated atia, along with high incidence of atrial fibrillation results in significant risk of intra-atrial thrombosis . However, free floating ball thrombus remains very rare in children. It is more common in patients with mitral valve stenosis and usually requires urgent surgical treatment . Development of free floating ball thrombus was rarely reported in patients with restrictive cardiomyopathy, even in sinus rhythm .
An 8-year-old girl who was diagnosed with idiopathic restrictive cardiomyopathy since the age of 4 years, and has a previous stroke was followed at our institution. She was on anticoagulation with war far in with a stable international normalized ratio of 2-3. She has severe ascites for which she was treated with abdominal paracentesis on a monthly basis. She presented with transient loss of vision. Her echocardiogram showed a large free floating left atrial thrombus (Figure 1). The thrombus was bouncing off the mitral valve with each ventricular systole in supplementary material (online movie). The patient had a fatal major thromboembolic event three days after the diagnosis of the ball thrombus.
This research received no specific grant from any funding agency, commercial, or not-for-profit sectors.
Conflict of Interest
Figure 1: An echocardiographic image in apical view of an eight year old child with severe restrictive cardiomyopathy. There is severe dilatation of both atria, and a large ball thrombus in the left atrium measuring 2.2 cm in diameter.
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