Atypical teratoid/rhabdoid tumor (AT/RT) is a Grade 4 embryonal tumor, rare and aggressive, most often presenting in children 0-5 years of age. In the adult population, AT/RTs are exceedingly rare, and usually located intracranially in the supratentorial compartment. AT/RTs of the spine are even more uncommon. Here, we detail the case of a young adult with AT/RT of the lumbar spine who underwent surgical resection of the lesion followed by radiation and chemotherapy. We also provide a comprehens...